Acrodermatitis EnteropathicaJune 3, 2017
Despite being the most common form of cutaneous T-cell lymphoma, mycosis fungoides (MF) is a rare disease. Rare case presentation has limited research and the clinical knowledge of physicians. Furthermore, vague dermatologic symptoms have led to frequent misdiagnosis and ill management.
MF is a mature T cell non-Hodgkin lymphoma that primarily develops in the skin, but can also involve lymph nodes, blood, and other organs. Clinically, MF typically begins as variably sized, pruritic, erythematous patches with a fine scale. Although a small percentage of MF patients may progress to developing patches, nodules, and/or gradually enlarging tumors that can undergo necrosis and ulceration, most patients with MF do not progress beyond patch- or plaque -type disease. Patients with MF typically have a prolonged clinical course.